Rib notching - Coarctation of aorta

Scimitar

CXR findings are that of a small lung with ipsilateral mediastinal shift, and in one third of cases the anomalous draining vein may be seen as a tubular structure paralleling the right heart border in the shape of a Turkish sword (“scimitar”).

Scimitar syndrome is associated with congenital heart disease, ipsilateral diaphragmatic anomalies and vertebral anomalies

Ebstein's anomaly

BOX SHAPED HEART

Septal and posterior leaflets of  the tricuspid valve are long and redundant  -and there proximal portion is plastered to the wall of RV particularly along septal wall - result in tricuspid regurgitation

- Proximal portion of RV cavity is “atrialized” but it contracts synchronously with the ventricle 

- RV performance markedly reduced

patent  fortamen  ovale or atrial  septal defect frequently seen - results in Rt-to-lt shunt  inducing central cyanosis